Caminati A, Cassandro R, Harari S (2013) Pulmonary hypertension in chronic interstitial lung diseases. Eur Respir Rev 22(129):292–301

Article  PubMed  PubMed Central  Google Scholar 

Raghu G, Amatto VC, Behr J, Stowasser S (2015) Comorbidities in idiopathic pulmonary fibrosis patients: a systematic literature review. Eur Respir J 46(4):1113–1130

Article  CAS  PubMed  Google Scholar 

DuBrock HM, Nathan SD, Reeve BB, Kolaitis NA, Mathai SC, Classi PM, Nelsen AC, Olayinka-Amao B, Norcross LN, Martin SA (2021) Pulmonary hypertension due to interstitial lung disease or chronic obstructive pulmonary disease: a patient experience study of symptoms and their impact on quality of life. Pulm Circ 11(2):20458940211005640

Article  PubMed  PubMed Central  Google Scholar 

Andersen CU, Mellemkjær S, Hilberg O, Nielsen-Kudsk JE, Simonsen U, Bendstrup E (2012) Pulmonary hypertension in interstitial lung disease: prevalence, prognosis and 6 min walk test. Respir Med 106(6):875–882

Article  PubMed  Google Scholar 

Lettieri CJ, Nathan SD, Barnett SD, Ahmad S, Shorr AF (2006) Prevalence and outcomes of pulmonary arterial hypertension in advanced idiopathic pulmonary fibrosis. Chest 129(3):746–752

Article  PubMed  Google Scholar 

Corte TJ, Keir GJ, Dimopoulos K et al (2014) Bosentan in pulmonary hypertension associated with fibrotic idiopathic interstitial pneumonia. Am J Respir Crit Care Med 190(2):208–217

Article  CAS  PubMed  PubMed Central  Google Scholar 

Nathan SD, Behr J, Collard HR et al (2019) Riociguat for idiopathic interstitial pneumonia-associated pulmonary hypertension (RISE-IIP): a randomised, placebo-controlled phase 2b study. Lancet Respir Med 7(9):780–790

Article  CAS  PubMed  Google Scholar 

Waxman A, Restrepo-Jaramillo R, Thenappan T et al (2021) Inhaled treprostinil in pulmonary hypertension due to interstitial lung disease. N Engl J Med 384(4):325–334

Article  CAS  PubMed  Google Scholar 

Rahaghi FF, Kolaitis NA, Adegunsoye A et al (2022) Screening strategies for pulmonary hypertension in patients with interstitial lung disease: a multidisciplinary Delphi study. Chest 162(1):145–155

Article  CAS  PubMed  PubMed Central  Google Scholar 

Nathan SD, Chandel A, Wang Y, Xu J, Shao L, Watkins TR, Diviney J, King CS, Han L (2024) Derivation and validation of a noninvasive prediction tool to identify pulmonary hypertension in patients with IPF: evolution of the model FORD. J Heart Lung Transp 43(4):547–553

Article  Google Scholar 

Parikh R, Konstantinidis I, O’Sullivan DM, Farber HW (2022) Pulmonary hypertension in patients with interstitial lung disease: a tool for early detection. Pulm Circ 12(4):e12141

Article  CAS  PubMed  PubMed Central  Google Scholar 

Zisman DA, Ross DJ, Belperio JA, Saggar R, Lynch JP 3rd, Ardehali A, Karlamangla AS (2007) Prediction of pulmonary hypertension in idiopathic pulmonary fibrosis. Respir Med 101(10):2153–2159

Article  PubMed  PubMed Central  Google Scholar 

Kovacs G, Bartolome S, Denton CP, Gatzoulis MA, Gu S, Khanna D, Badesch D, Montani D (2024) Definition, classification and diagnosis of pulmonary hypertension. Eur Respir J 64:2401324

Article  CAS  PubMed  PubMed Central  Google Scholar 

Simonneau G, Montani D, Celermajer DS, Denton CP, Gatzoulis MA, Krowka M, Williams PG, Souza R (2019) Haemodynamic definitions and updated clinical classification of pulmonary hypertension. Eur Respir J 53(1):1801913

Article  CAS  PubMed  PubMed Central  Google Scholar 

Hoeper MM, Bogaard HJ, Condliffe R, Frantz R, Khanna D, Kurzyna M, Langleben D, Manes A, Satoh T, Torres F, Wilkins MR, Badesch DB (2013) Definitions and diagnosis of pulmonary hypertension. J Am Coll Cardiol 62(25):D42-50

Article  PubMed  Google Scholar 

Raghu G, Remy-Jardin M, Myers JL et al (2018) Diagnosis of idiopathic pulmonary fibrosis. An official ATS/ERS/JRS/ALAT clinical practice guideline. Am J Respir Crit Care Med 198(5):e44–e68

Article  PubMed  Google Scholar 

Parikh R, O’Sullivan DM, Farber HW (2023) The PH-ILD detection tool: external validation and use in patients with ILD. Pulm Circ 13(3):e12273

Article  CAS  PubMed  PubMed Central  Google Scholar 

Nathan SD, Shlobin OA, Ahmad S, Urbanek S, Barnett SD (2007) Pulmonary hypertension and pulmonary function testing in idiopathic pulmonary fibrosis. Chest 131(3):657–663

Article  PubMed  Google Scholar 

Rose L, Prins KW, Archer SL, Pritzker M, Weir EK, Misialek JR, Thenappan T (2019) Survival in pulmonary hypertension due to chronic lung disease: Influence of low diffusion capacity of the lungs for carbon monoxide. J Heart Lung Transp 38(2):145–155

Article  Google Scholar 

Shorr AF, Wainright JL, Cors CS, Lettieri CJ, Nathan SD (2007) Pulmonary hypertension in patients with pulmonary fibrosis awaiting lung transplant. Eur Respir J 30(4):715–721

Article  CAS  PubMed  Google Scholar 

Braganza M, Shaw J, Solverson K, Vis D, Janovcik J, Varughese RA, Thakrar MV, Hirani N, Helmersen D, Weatherald J (2019) A prospective evaluation of the diagnostic accuracy of the physical examination for pulmonary hypertension. Chest 155(5):982–990

Article  PubMed  Google Scholar 

Mar PL, Nwazue V, Black BK, Biaggioni I, Diedrich A, Paranjape SY, Loyd JE, Hemnes AR, Robbins IM, Robertson D, Raj SR, Austin ED (2016) Valsalva maneuver in pulmonary arterial hypertension: susceptibility to syncope and autonomic dysfunction. Chest 149(5):1252–1260

Article  PubMed  PubMed Central  Google Scholar 

Lama VN, Flaherty KR, Toews GB, Colby TV, Travis WD, Long Q, Murray S, Kazerooni EA, Gross BH, Lynch JP 3rd, Martinez FJ (2003) Prognostic value of desaturation during a 6-minute walk test in idiopathic interstitial pneumonia. Am J Respir Crit Care Med 168(9):1084–1090

Article  PubMed  Google Scholar 

Paciocco G, Martinez FJ, Bossone E, Pielsticker E, Gillespie B, Rubenfire M (2001) Oxygen desaturation on the six-minute walk test and mortality in untreated primary pulmonary hypertension. Eur Respir J 17(4):647–652

Article  CAS  PubMed  Google Scholar 

Keir GJ, Wort SJ, Kokosi M et al (2018) Pulmonary hypertension in interstitial lung disease: limitations of echocardiography compared to cardiac catheterization. Respirology 23(7):687–694

Article  PubMed  Google Scholar 

Ramspek CL, Jager KJ, Dekker FW, Zoccali C, van Diepen M (2021) External validation of prognostic models: what, why, how, when and where? Clin Kidney J 14(1):49–58

Article  PubMed  Google Scholar 

Van Calster B, McLernon DJ, van Smeden M, Wynants L, Steyerberg EW (2019) Calibration: the Achilles heel of predictive analytics. BMC Med 17(1):230

Article  PubMed  PubMed Central  Google Scholar 

Habib G, Torbicki A (2010) The role of echocardiography in the diagnosis and management of patients with pulmonary hypertension. Eur Respir Rev 19(118):288–299

Article  CAS  PubMed  PubMed Central  Google Scholar 

Furukawa T, Kondoh Y, Taniguchi H, Yagi M, Matsuda T, Kimura T, Kataoka K, Johkoh T, Ando M, Hashimoto N, Sakamoto K, Hasegawa Y (2018) A scoring system to predict the elevation of mean pulmonary arterial pressure in idiopathic pulmonary fibrosis. Eur Respir J 51(1):1701311

Article  PubMed  Google Scholar 

Sobiecka M, Lewandowska K, Kober J, Franczuk M, Skoczylas A, Tomkowski W, Kuś J, Szturmowicz M (2020) Can a new scoring system improve prediction of pulmonary hypertension in newly recognised interstitial lung diseases? Lung 198(3):547–554

Article  CAS  PubMed  PubMed Central  Google Scholar 

Bax S, Bredy C, Kempny A et al (2018) A stepwise composite echocardiographic score predicts severe pulmonary hypertension in patients with interstitial lung disease. ERJ Open Res 4(2):00124